Clinical and laboratory observationPancreatitis in young children with cystic fibrosis
References (12)
- et al.
Acute pancreatitis in children
J Pediatr
(1988) Gastrointestinal manifestations of cystic fibrosis
Pediatr Clin North Am
(1975)- et al.
Protease-specific suppression of pancreatic exocrine secretion
Gastroenterology
(1984) - et al.
The pancreas: clinical aspects and investigation of pancreatic function
- et al.
Recurrent acute pancreatitis in patients with cystic fibrosis with normal pancreatic enzymes
Pediatrics
(1975) The pathophysiology of the pancreatic defect in cystic fibrosis
Acta Paediatr Scand Suppl
(1989)
Cited by (60)
Cystic Fibrosis and Congenital Anomalies of the Exocrine Pancreas
2020, Pediatric Gastrointestinal and Liver Disease, Sixth EditionHow are the ancient cystic fibrosis patients? Cystic fibrosis diagnosed over 60 years-old
2017, Respiratory Medicine Case ReportsCitation Excerpt :Other causes leading to diagnosis found in our study were male sterility, allergic bronchopulmonary aspergillosis (ABPA) and recurrent respiratory infections. None of our patients have recurrent pancreatitis, despite that being one of the most common clinical manifestations and diagnostic suspicions in other series, both children and adults with CF [7,15,16]. Thus, CF should also be considered a disease to be diagnosed in adulthood, including the sweat test within the usual tests of differential diagnosis in patients with diseases, such as bronchiectasis or chronic bronchial infection of unknown etiology.
Chronic Pancreatitis
2016, Surgical Pathology ClinicsCitation Excerpt :In the vast majority of patients, exocrine pancreatic insufficiency occurs in utero or soon after birth. However, minor CFTR mutations have been identified in children and young adults with idiopathic chronic pancreatitis, in the absence of other organ manifestations of this disease.49 In addition to PRSS1 and CFTR, mutations in SPINK1 have also been shown to be associated with hereditary and idiopathic chronic pancreatitis.50
CFTR and/or pancreatitis susceptibility genes mutations as risk factors of pancreatitis in cystic fibrosis patients?
2016, PancreatologyCitation Excerpt :Acute pancreatitis (AP) or recurrent AP (RAP) is an infrequent complication of CF that was first mentioned by Shwachman et al. [5]. The occurrence of pancreatitis among CF patients was estimated to be between 0.5% and 1.7% [5–8]. Only CF patients with PS are at risk of pancreatitis [6,7].
Cystic fibrosis in adult age
2014, Revista Clinica EspanolaCystic Fibrosis and Congenital Anomalies of the Exocrine Pancreas
2011, Pediatric Gastrointestinal and Liver Disease