Table 1

Underlying conditions in patients with systemic AA amyloidosis

Condition No of patients (%)
Juvenile rheumatoid arthritis50  (36)
Rheumatoid arthritis40 (29)
Chronic sepsis9 (6.5)
Familial Mediterranean fever7 (5.1)
Tuberculosis6 (4.3)
Crohn’s disease5 (3.6)
Castleman’s disease1-150 3 (2.2)
Ankylosing spondylitis2 (1.4)
Epidermolysis bullosa congenita1-150 1 (0.7)
Familial Hibernian fever1-150 1 (0.7)
Intravenous drug misuse1 (0.7)
Paraplegia1 (0.7)
Psoriatic arthropathy1 (0.7)
Polyarteritis nodosa1 (0.7)
Peritoneal mesothelioma1-150 1 (0.7)
Muckle-Wells syndrome1 (0.7)
Systemic vasculitis1 (0.7)
Not known1-150 7 (5.1)
  • 1-150 Conditions in which systemic AA amyloidosis is not widely recognised as a complication.