Reference | Sex | Age at first symptoms of PIL (y) | Lymphocyte counts (μl) | Cutaneous warts | Time from PIL to lymphoma onset (y) | Lymphoma | Outcome | ||||||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Location | Type | Treatment | Lymphoma | Enteropathy | |||||||||||||
Waldman 19724 (3 cases) | NS | NS | NS | NS | 3, 22 and 25 | Breast, | NS | NS | ? | ? | |||||||
small bowel, | NS | NS | ? | ? | |||||||||||||
stomach | NS | NS | ? | ? | |||||||||||||
Ward 19776 | M | 12 | 1000 | + | 27 | Jejunum | NS (lymphocytic) | Surgery, radiotherapy | Death | ||||||||
Broder 19817 1-a | F | 24 | 600 | NS | 15 | Breast | B cell (small cells) | CVP1-b | Complete remission | Improved | |||||||
Case record 19848 | F | 57 | 798 | NS | 13 | GI tract | B cell (immunoblasts) | VCP1-c | Death | ||||||||
Herait 19859 | F | 3 | 860 | NS | 15 | Retroperitoneum, mediastinum | NS (large cells) | AVmCP1-d | Complete remission | Unchanged | |||||||
Shpilberg 199310 | F | 6 | 640 | NS | 13 | Bone | B cell (large cells) | CHOP1-e, radiotherapy | Complete remission | Improved | |||||||
Guma 199811 | F | 34 | NS | + | 20 | Jejunum | B cell (large cells) | Surgery, CHOP | Complete remission | Unchanged | |||||||
Present case 1 | F | 11 | 700 | + | 39 | Midgut | B cell (centoblastic) | Surgery, AVmCP | Complete remission | Unchanged | |||||||
Present case 2 | F | 18 | 990 | + | 40 | Ileum | B cell (centoblastic) | PACOB1-f | Complete remission | Unchanged |
↵1-a There is some evidence that this case is one of the initial three cases quoted by Waldman and colleagues4;
↵1-b cyclophosphamide, vincristine, prednisone;
↵1-c vincristine, chlorambucil, prednisone;
↵1-d adriamycin, teniposide, cyclophosphamide, prednisone;
↵1-e cyclophosphamide, adriamycin, vincristine, prednisone;
↵1-f prednisolone, adriamycin, cyclophosphamide, vincristine, bleomycin.
+, present; NS, not stated; M, male; F, female.