Table 4

Disease characteristics of the colonic adenomatous APC mutation negative families

Family No Age at
diagnosis (y)
Age at cancer
diagnosis (y)
No affected relatives
(age at diagnosis)
Other cancers in
relatives (age)
1226 (21, 26, 28,52, 40, ?)None reported
24743,542 (40+4-150, 40+4-150)None reported
3226 (22, 25, 61, ?, ?, ?)None reported
433330None reported
5410None reported
652520None reported
7232 (44, 20)None reported
838471 (57)Melanoma (42)
0Unknown cancer
9410None reported
10241 (29)None reported
1113140None reported
1283 (19, 20, 39)Desmoid disease
1362620None reported
14535 (19, 22, 26, 42, ?)None reported
1541410None reported
16415 (24, ?, ?, ?, ?)None reported
17722 (63, 78)Skin cancer (?),
laryngeal cancer (?)
  • ? Unknown age.

  • 4-150 Exact age not available.