Table 2

Features and outcome of the 17 patients in our series. Group 1, patient Nos 1–4; group 2, patient Nos 5–17

Patient NoYearAge (y)SexEncephalopathy at admissionD-penicillamine administrationLiver transplantationOutcome
119698FNoNoNoDead
2197013MNoNoNoDead
3197115FNoNoNoDead
4197215FNoNoNoDead
5198719MYesNoYesDead
6198910FYesNoYesAlive
7197921MNoYesNoAlive
8198317MNoYesNoAlive
9198320FNoYesNoAlive
10198516FNoYesNoAlive
11198817FNoYesNoAlive
12198817FNoYesNoAlive
13198922FNoYesNoAlive
14199016FNoYesYesAlive
15199021FNoYesNoAlive
16199119MNoYesNoAlive
17199917FNoYesNoAlive