Table 1

Demographic and clinical findings

SubjectSexAge (y)Final diagnosisDuration of dysphagia prior to evaluation (months)Presentation to diagnosis of cause of dysphagia (months)Head and neck muscle involvementMuscle weaknessAspirationDysphagia severityUOS restrictive feature
*Patient did not undergo pharyngeal videomanometry.
UOS, upper oesophageal sphincter.
Idiopathic presentation
1F81Polymyositis1800.46NoNoNoMildYes
2F59Polymyositis7211NoNoYesMildYes
3F74Polymyositis240.23YesProximalYesSevereYes
4F67Polymyositis60.23NoProximalYesModerateNo
5M69Polymyositis3645NoNoYesMildYes
6M75Interstitial myositis110.46YesYesYesSevereNo
7M74Polymyositis190.7YesProximalNoMildYes
8F88Polymyositis1440.06YesProximalYesMod-sevYes
9*F22Polymyositis10.23NoProximalNoNo
Confirmed myopathy at time of referral
10M45Inclusion body myositis18Prior 4 monthsYesProximal limbNoMildYes
11M71Dermatomyositis16Prior 10 yearsNoProximal limbYesMildNo
12F86Polymyositis24Prior 4 yearsNoProximal limbNoMild-ModYes
13F74Polymyositis360.46YesProximal, facialYesSevereYes