Table 1

Clinical details of patients at referral

Patient 1 Patient 2 Patient 3 Patient 4 Patient 5
SexFemaleFemale FemaleMaleFemale
Age5450405847
family history++++
TelangiectasiaFaceFaceFaceFaceFace
Epistaxis+++
Clinical symptoms of complicationsDyspnoeaUpper GI bleedingAbdominal anginaDyspnoeaVitality decrease
NycturiaLeft ventricular hypertrophyWeight lossNycturiaDyspnoea
Left ventricular hypertrophyMitral insufficiencyTricuspidal insufficiencyVitality decrease
ArrhythmiaAscitesVentricular extrasystoles
HypertensionCongested jugular veins
AscitesSteal syndrome
Hepatomegaly+++++
Bruit over the liver+++++
Alkaline phosphatase raised+++++
GGT raised+++++
Cardiac output (l/min) before therapy1517,3131212.5
ShuntArteriovenousArterioportalArteriovenousArteriovenousArteriovenous
Number of embolisations33533
  • GGT, γ-glutamyl transferase; GI, gastrointestinal.