Table 3

Clinical features of patients with hereditary pancreatitis in two families with the gene mutation in cationic trypsinogen

Subject number Family numberAgeSexIdentified mutationAge of onsetSymptomsPancreatic configurationPancreatic calcificationDiabetes mellitusRemarks on clinical course
1015100069MExon 316MildPseudocyst++
1034100058MExon 36MildDilatation of MPD+
1049100049FExon 35SevereMarked dilatation of MPD+Open surgery due to acute pancreatitis (at 13 years)
6045600053FExon 234MildMarked dilatation of MPD+Longitudinal pancreatico-jejunostomy (at 37 years)
6046600061FExon 228MildMarked dilatation of MPD++Longitudinal pancreatico-jejunostomy (at 46 years)
  • MPD, main pancreatic duct.