Location, association with multiple endocrine neoplasia (MEN1), and incidence of less rare types of pancreatic neuroendocrine tumours
| Metastases >(%) | % MEN1 | Incidence per year | |
|---|---|---|---|
| *Approximately half of the cases arise in the duodenum. | |||
| †Also arise in the lungs and jejunum. | |||
| ‡Occasionally arise elsewhere. | |||
| Insulinoma | 10 | 5 | 1–2/million |
| Gastrinoma* | 60 | 25–40 | 1–2/million |
| Glucagonoma | 50–80 | 10 | 0.1/million |
| VIPoma | 40–70 | 5 | 0.1/million |
| Somatostatinoma* | 70 | 45 | <0.1/million |
| Ectopic GRFoma† | 60–70 | 15 | <0.1/million |
| Ectopic ACTHoma‡ | 90 | <5 | <0.1/million |
| Non-syndromic | 60 | 20 | 1–2/million |