Table 2

 Features of 43 patients with primary biliary cirrhosis-systemic sclerosis (PBC-SSc)

PBC-SSc
Values are number (%) or median (range).
Limited cutaneous SSc (lcSSc)40 (93%)
Diffuse cutaneous SSc (dcSSc)3 (7%)
SSc diagnosed before PBC24 (56%)
Time interval between diagnosis of SSc and PBC (y)4.87 (0.06–26.7)
PBC diagnosed before SSc19 (44%)
Time interval between diagnosis of PBC and SSc (y)4.08 (0.30–13.7)