Patient no. | Age at onset | Sex | Obstructive jaundice | Abdominal pain | Pancreatic ductal change | Total bilirubin (m g/dl) | Alkaline phosphatase (IU/l) | IgG4 (mg/dl) | BT–PABA (%) | Initial dose of PSL (mg) | Cessation of CST (months after initiation) | Event during follow -up | Period to event occurence or observation period (months) |
1 | 70 | F | + | – | Diffuse | 5.8 | 1643 | 133 | 40 | – | IP | 26 | |
2 | 57 | M | + | – | Diffuse | 10.6 | 418 | 25 | 29 | IP | 45 | ||
3 | 75 | M | + | – | Diffuse | 6.7 | 1427 | 354 | 30 | – | IP | 15 | |
4 | 63 | M | + | + | Local | 3.0 | 850 | 691 | 45 | 30 | – | OJ | 4 |
5 | 58 | M | + | + | Local | 9.2 | 2744 | 50 | 5 | OJ | 22 | ||
6 | 61 | M | – | – | Local | 0.4 | 740 | 410 | 40 | – | OJ | 27 | |
7 | 69 | F | – | + | Diffuse | 0.4 | 996 | 249 | 54 | 40 | – | None | 72 |
8 | 66 | M | + | + | Local | 5.3 | 2299 | 525 | 75 | 40 | – | None | 56 |
9 | 55 | M | + | + | Diffuse | 1.7 | 222 | 320 | 40 | – | None | 53 | |
10 | 66 | M | – | + | Diffuse | 0.5 | 113 | 310 | 30 | – | None | 54 | |
11 | 73 | M | + | + | Local | 5.4 | 1041 | 360 | 50 | 30 | – | None | 49 |
12 | 72 | F | + | – | Diffuse | 1.6 | 1968 | 1400 | 44 | 30 | – | None | 36 |
13 | 61 | M | + | + | Local | 1.6 | 1290 | 578 | 63 | 30 | – | None | 27 |
14 | 58 | M | + | – | Diffuse | 6.9 | 1004 | 481 | 30 | – | None | 21 | |
15 | 71 | M | – | – | Local | 0.6 | 420 | 470 | 30 | – | None | 15 | |
16 | 55 | M | + | – | Diffuse | 2.9 | 728 | 30 | – | None | 13 | ||
17 | 61 | M | – | + | Local | 0.5 | 217 | 974 | 64 | 30 | – | None | 15 |
18 | 65 | M | + | + | Local | 5.4 | 481 | 1260 | 30 | – | None | 12 | |
19 | 64 | M | – | – | Diffuse | 0.4 | 171 | 361 | 36 | 30 | – | None | 11 |
BT–PABA, N-benzoyl-l-tyrosyl-p-aminobenzoic acid test >70% normal; IP, interstitial pneumonia; OJ, obstructive jaundice caused by intrapancreatic bile duct stenosis; PSL, prednisolone. Normal range: Total bilirubin, 0.3–1.3 mg/dl; alkaline phosphatase, 60–201 IU/l; IgG4, <135 mg/dl.