Table 2

Location, likelihood of metastasis and association with MEN1 in NETs21 22

Tumour% Metastases% MEN1Incidence per million per year
Insulinoma1051–2
Gastrinoma*6025–401–2
Glucagonoma50–80100.1
VIPoma40–7050.1
Somatostatinoma*50–7045<0.1
Non-syndromic60201–2
  • * About half of cases arise in the duodenum.

  • MEN1, multiple endocrine neoplasia 1; NET, neuroendocrine tumour; VIPoma, vasoactive intestinal peptide-secreting tumour.