Distribution of disease relapse episodes according to initial treatment strategies, and location and frequency for those treated with steroids
| Type 1 AIP | Type 2 AIP | |||
|---|---|---|---|---|
| Relapse, n | % | Relapse, n | % | |
| Initial treatment | ||||
| Steroids | 245/684 | 35.8 | 8/52 | 15.3 |
| Surgical resection | 35/116 | 30.2 | 0/25 | 0 |
| Palliative surgical bypass | 11/23 | 47.8 | 0/2 | 0 |
| Conservative | 11/57 | 19.3 | 0/6 | 0 |
| Disease relapses following steroid treatment | ||||
| Location of relapse | n=245 episodes | n=8 episodes | ||
| Biliary system | 124 | 50.6 | – | – |
| Pancreas | 107 | 42.9 | 8 | 100 |
| Salivary | 18 | 7.3 | – | – |
| Lung | 11 | 4.5 | – | – |
| Lymphadenopathy | 4 | 1.6 | – | – |
| Renal | 3 | 1.2 | – | – |
| Other (RPF or NOS) | 13 | 5.3 | – | – |
| Frequency per subject | ||||
| One relapse | 189 | 77.1 | 8 | 100 |
| Two relapses | 39 | 15.9 | – | – |
| Three relapses | 13 | 5.3 | – | – |
| ≥4 relapses | 4 | 1.6 | – | – |
AIP, Autoimmune pancreatitis; RPF, retroperitoneal fibrosis; NOS, not otherwise specified.