Table 1

Diseases associated with autoimmune hepatitis (AIH)

DiseaseReferencesPrevalence in AIH (%)
Primary biliary cirrhosis764–14
Primary sclerosing cholangitis76–782–8
Inflammatory bowel disease10 63 79–812–8
Coeliac disease10 62 82–851–2
Rheumatoid arthritis62 862–5
Mixed connective tissue disease622.5
Sjogrens10 62 871–4
Systemic lupus erythematosus10 62 881–2
Fibrosing alveolitis89
Glomerulonephritis90
Thrombocytopenia91
Haemolytic anaemia92
Thyroiditis10 61 6210–23
Diabetes107–9
Psoriasis103
Vitiligo93
Glomerulonephritis101
Uveitis94
Polymyositis95
Multiple sclerosis62 961
Mononeuritis multiplex97
Antiphospholipid syndrome98