Table 1

Clinical characteristics of nine patients with IgG4-RD and reactivity against a 56 kDa protein

Patient	Age at diagnosis	Gender	Organ involvement	Diabetes	serum IgG4 (ULN=1.4 mg/mL)	IgG4/IgG RNA ratio (ULN=5%)	Response to prednisolone	IgG4 reactivity on western blot	IgG1 Reactivity on western blot
IRD1	52	M	IAC, AIP, GLA	+	6,17	24,92	+	+	+
IRD2	53	M	IAC, AIP, kidney	+	4,89	15,89	ND	+	+
IRD3	74	F	IAC, AIP	+	8,82	51,51	+	+	+
IRD4	69	M	IAC, kidney, LLA	+	8,10	24,63	+	+	+
IRD5	49	M	IAC, AIP, orbits, SMG	+	14,60	30,02	+	+	+
IRD6	66	M	IAC, AIP	+	2,98	9,36	+	+	+
IRD7	64	M	IAC, LLA	-	1,74	6,89	+	+	+
IRD8	80	M	IAC, AIP, larynx	-	1,40	26,04	+	+	-
IRD9	49	M	IAC, AIP, LLA	-	3,75	9,63	ND	+	-

AIP , autoimmune pancreatitis; GLA, generalised lymphadenopathy; IAC, immunoglobulin G4-associated cholangitis; IRD, immunoglobulin G4-RD; LLN, localised lymphadenopathy; ND, not done; SMG, submandibular glands; ULN, upper limit of normal.