Summary
This report documents the occurrence of hepatocellular carcinoma in a 36-year-old man with arteriohepatic dysplasia and a noncirrhotic liver. This case represents one of the oldest patients reported to have arteriohepatic dysplasia and the first with the development of a hepatocellular carcinoma, of which I am aware. Although this tumor has been reported with other familial cholestatic syndromes, the absence of an underlying cirrhosis is of particular interest.
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Adams, P.C. Hepatocellular carcinoma associated with arteriohepatic dysplasia. Digest Dis Sci 31, 438–442 (1986). https://doi.org/10.1007/BF01311683
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DOI: https://doi.org/10.1007/BF01311683